Hong Kong Med J 2013;19:174–7 | Number 2, April 2013
Degos' syndrome complicated by bowel perforation: focus on radiological findings
Jessie TH Yeung, Johnny KF Ma, Alfred WT Yung
Department of Diagnostic Radiology, Princess Margaret Hospital, Laichikok, Hong Kong
We describe a 50-year-old man who first presented with multiple skin lesions which were characteristic of Degos' syndrome. The patient developed multiple episodes of abdominal pain. Some episodes resolved with conservative management, for others he underwent urgent operations for bowel perforations. The patient subsequently underwent extensive small bowel resection, but further systemic deterioration ensued and he died. The imaging findings of Degos' syndrome and the implications of pneumatosis intestinalis and pneumoperitoneum are discussed.
Key words: Intestinal perforation; Malignant atrophic papulosis; Pneumatosis cystoides intestinalis; Pneumoperitoneum; Skin diseases, vascular
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